Fibro-osseous lesions are frequently found in facial bones, especially in mandible and maxilla. Their origin is periodontal membrane which is composed with collagen fiber, mucopolysaccharide, oxytalan fiber and mesenchymal blastic cells. Among them, mesenchymal blastic cell forms cementum, lamella bone and fibrous tissue, especially in many pathologic conditions. But the causes are not certainly known until now.
All cementoid lesions were frequently called as cementoma until 1971, when WHO classified cementoid lesions as followings; benign cementoblastoma, cementifying fibroma, periapical cemental dysplasia and gigantiform cementoma. In 1968, Hamner summarized 148 cases of cementoid lesions statistically. Their mean age of onset was 36 years old and he reported 18% of multiple lesions and 3 cases of giant lesion, but which were not greater than 2cm. in diameter.
We experienced a patient whose clinical features have not been found in any other literatures.
The clinical features are as followings:
1. Early onset; first noted at 3 years old.
2. Multiple lesion; maxilla and mandible are involved bilaterally.
3. Rapid growing; within 4 month, mass enlarged to 10cm. in dia.
4. Familial involvement; mother and aunt are suffered from same lesions in mandible and vertex.
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